Conservative management of multiple keratocystic odontogenic tumours in a child with Gorlin-Goltz syndrome: a case report.

نویسندگان

  • C Wilson
  • M Murphy
چکیده

BACKGROUND The recommendations regarding the management of keratocystic odontogenic tumour (KCOT) vary widely in the literature. The authors highlight that conservative surgical management should still be considered in some cases. CASE REPORT A young patient with Gorlin-Goltz Syndrome and two large mandibular KCOTs is presented. The case demonstrates conservative treatment with enucleation of the tumours and preservation of all involved teeth. Subsequent orthodontic treatment resulted in all teeth erupting successfully. The tumour cavities regenerated with bone.

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

منابع مشابه

Conservative Management of Ovarian Fibroma in A Case of Gorlin-Goltz Syndrome Comorbid with Endometriosis

Ovarian fibromas are the most common benign solid ovarian tumors, which preoperative diagnosis often is difficult. Ovarian fibromas, especially in bilateral cases, may be representative of Gorlin syndrome.Gorlin syndrome (GS) is a rare autosomal dominant disorder with predisposition to basal cell carcinomas (BCCs) and other various benign and malignant tumors. To report a case of a young patien...

متن کامل

Multiple, multifocal odontogenic keratocysts in non-syndrome patient: a case-report.

Occurrence of multiple odontogenic keratocyst involving the jaws is rare. When multiple, it is usually associated with a syndrome. Occurrence of multiple odontogenic keratocyst without syndromic association is extremely rare. Gorlin-Goltz syndrome which is also known as Nevoid Basal Cell Carcinoma Syndrome is a rare autosomal dominant disorder. Multiple Odontogenic Keratocysts (OKCs) are princi...

متن کامل

Gorlin Syndrome with Bilateral Polydactyly: A Rare Case Report

Gorlin's syndrome is a rare disorder transmitted as an autosomal dominant trait. It is characterized by multiple disorders involving multiple systems. We present a case of 11-year-old male child presenting with multiple odontogenic keratocyst to the dental clinic. Retrograde diagnosis of Gorlin-Goltz syndrome was made after clinical and radiological investigation. How to cite this article: Acha...

متن کامل

Removal of Multiple Keratocystic Odontogenic Tumors in a Nonsyndromic Patient

Multiple keratocystic odontogenic tumors are one of the key features of Gorlin-Goltz syndrome. A 15-year-old nonsyndromic female child presented with multiple keratocystic odontogenic tumors. The presence of the tumors was observed in immunological examinations. The images led to the suspicion of Gorlin-Goltz syndrome which was discarded after analyzing the patient's medical history and complem...

متن کامل

Gorlin-Goltz syndrome: A rare case report

Gorlin-Goltz syndrome (GS), also known as nevoid basal cell carcinoma syndrome, is an infrequent multisystem disease inherited in a dominant autosomal way, which shows a high level of penetrance and variable expressiveness. It is characterised by keratocystic odontogenic tumours (KCOT) in the jaw, multiple basal cell nevi carcinomas and skeletal abnormalities. This syndrome may be diagnosed ear...

متن کامل

ذخیره در منابع من


  با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

عنوان ژورنال:
  • European journal of paediatric dentistry : official journal of European Academy of Paediatric Dentistry

دوره 9 4  شماره 

صفحات  -

تاریخ انتشار 2008